Primary renal carcinoid tumor (PRCT) is extremely rare since normally no enterochromaffin cells will be found in renal parenchyma. The clinical manifestations of PRCT are often non-specific, sometimes even without symptoms. There were about 90 cases reported in the literatures to our knowledge. We reported a PRCT in a 67-year-old woman, which was incidentally found in the health examination. The literature was reviewed. We suggest that PRCT should be considered when a renal tumor coexists with horseshoe kidney or a renal mass shows hypovascularity on the angiography.