Fulminant Pulmonary Hemorrhage as the Initial Manifestation in Systemic Lupus Erythematosus: A Case Report and Review of the Literature

以猛暴性肺出血為最初表現之全身性紅斑性狼瘡：－病例報告與文獻回顧

林建亨(Chien-Heng Lin) ； 賴慶鴻(Ching-Hong Lai) ； 林維卿(Wei-Ching Lin) ； 巫康熙(Kang-His Wu) ； 陳安琪(An-Chyi Chen) ； 林鴻志(Hung-Chih Lin) ； 張正成(Jeng-Sheng Chang)

《中華民國兒童胸腔醫學會雜誌》 5卷2期 (2006/07) Pp. 81-88

https://doi.org/10.6322/JPRD.200607_5(2).0005

摘要

肺出血是全身性紅斑性狼瘡病患一種不常見的臨床表現。以猛暴性肺出血為最初表現在全身性紅斑性狼瘡之兒科病患是罕見的而且死亡率很高。我們在此報告一位十六歲的女孩一開始表現猛暴性肺出血，之後被診斷是全身性紅斑性狠瘡，並且成功地以早期積極的脈衝性類固醇及免疫抑制劑治療。肺出血可以是全身性紅斑性狠瘡之最初表現，早期診斷且立即地給予重症加護治療是成功拯救全身性紅斑性狼瘡病患合併猛暴性肺出血的原則。

關鍵字

肺出血 ； 全身性紅斑性狼瘡

並列摘要

Pulmonary hemorrhage is an unusual clinical manifestation of systemic lupus erythromatosus (SLE). Fulminant pulmonary hemorrhage as the initial manifestation of SLE in pediatric patients is rare and the mortality rate is high. We report a 16 year-old female who initially presented with fulminant pulmonary hemorrhage; she was diagnosed as having SLE and was successfully treated by early aggressive management with methylprednisolone and cyclophosphamide pulse therapies. It is important to keep in mind that pulmonary hemorrhage can be the initial presentation of SLE. Early diagnosis and rapid intensive care arc necessary to successfully rescue SLE patients with fulminant pulmonary hemorrhage.

並列關鍵字

pulmonary hemorrhage ； systemic lupus erythematosus