- 期刊
大前庭導水管症候群－病例報告
Large Vestibular Aqueduct Syndrome – Case Report
摘要
隨著高解析度電腦斷層掃瞄與磁振造影的廣泛使用，大前庭導水管是目前影像診斷學上常見的內耳畸形之一，大多數伴隨有出生後或幼兒早期的感音神經性聽力損失，部份併有傳音性聽力損失，但只極少數呈現聽力正常。大前庭導水管症候群通常是兩側性的，聽力損失呈現階梯狀的進展，而前庭導水管的大小與與聽力損失的程度、型態或惡化速率並無相關性存在 我們經驗1例現年11歲的女孩，過去有多次突發性的感音神經性聽力喪失，高解析度電腦斷層掃瞄顯示兩側前庭導水管異常擴大，經治療後繼續追蹤聽力變化，而患者之漸進性聽力惡化並未因手術施行而減緩。
並列摘要
Large vestibular aqueduct (LVA) is a common inner ear malformation. Sensorineural hearing loss, sometimes combined with a conductive component, is the predominant feature of LVA syndrome. Very few patients with LVA have normal hearing. Hearing loss is usually noted after birth or during the early childhood. LVA usually occurs bilaterally and there is a slight female predominance. The size of the vestibular aqueduct does not relate to the degree, type or rate of progression of hearing loss. At present no treatment has been found to halt the progression of hearing loss. Early detection of LVA in patients with sensorineural hearing loss of unknown etiology is essential for better prognosis. We herein present an 11 year-old girl with several episodes of fluctuating sensorineural hearing loss noted since her age of 3 years. High resolution computed tomography of the temporal bones revealed bilateral large vestibular aqueducts. She developed progressive hearing loss despite surgical intervention. Her latest audiogram showed bilateral profound sensorineural hearing loss.
延伸閱讀
- 林鴻清（2005）。前庭導水管擴大症後群。聽障教育期刊，(4)，21-24。https://www.airitilibrary.com/Article/Detail?DocID=P20151125002-200512-201512010023-201512010023-21-24
- Huang, L. H., Huang, Z. M., Tung, M. Z., & Tsao, T. Y. (2017). 結節狀組織球前列腺炎：一病例報告及文獻回顧. 童綜合醫學雜誌, 11(2), 131-134. https://www.airitilibrary.com/Article/Detail?DocID=20713592-201712-201805170014-201805170014-131-134
- Chang, H. C., CHerng, Y. G., Lee, T. S., Lin, C. J., Tai, Y. T., Chen, T. G., & Chen, T. L. (1999). HELLP症候群合併産前肺水腫－病例報告. Acta Anaesthesiologica Sinica, 37(1), 41-44. https://doi.org/10.6955/AAS.199903.0041
- Huang, K. S., Cheung, K. S., Chen, Y. S., Ma, C. L., Man, K. M., & Wang, L. C. (2014). 骨水泥植入症候群：一病例報告及文獻回顧. 童綜合醫學雜誌, 8(1), 31-36. https://www.airitilibrary.com/Article/Detail?DocID=20713592-201406-201409090010-201409090010-31-36
- 吳鳳旗、賴仁淙、李袓信、洪俊光（1997）。Retrosigmoid Vestibular Neurectomy。中華民國耳鼻喉科醫學會雜誌，32(5)，402-407。https://doi.org/10.6286/1997.32.5.402