Management of Multiple Impacted Supernumerary Teeth of an Adult Patient with Cleidocranial Dysplasia - A Case Report

鎖骨顱骨發育不良患者之多發性阻生贅生齒處置－病例報告

何宗訓(Tsung-Hsun Ho) ； 章浩宏(Hao-Hueng Chang)

《中華民國家庭牙醫學雜誌》 15卷2期 (2020/09) Pp. 16-24

https://doi.org/10.6566/JFD.202009_15(2).0003

摘要

Cleidocranial dysplasia is a rare autosomal dominant genetic disease, and affects about one per million people. Due to the mutation of gene for specific osteoblast transcription factor, the development of bone and cartilage is effected, and result in calvarial, craniofacial and clavicular abnormality. The oral and dental features include delayed or ectopic eruption of permanent dentition, multiple supernumerary teeth, delayed root resorption of deciduous teeth, dilacerations of permanent and supernumerary teeth, and malocclusion. This case report presents a 28-year-old woman complained about malalignment of her dentition. She had 14 deciduous teeth failed to exfoliate and only 11 permanent teeth erupted. Radiographic examination showed there were 21 impacted permanent teeth and 18 impacted supernumerary teeth in her jaw bones. The patient had Angle's Class III malocclusion and had orthodontic evaluation. Then she was referred to oral maxillofacial surgery department for odontectomy of impacted supernumerary teeth and surgical exposure of impacted permanent teeth under general anesthesia. Simultaneously, orthodontic appliance was placed and forced eruption was started right after the surgery.

關鍵字

cleidocranial dysplasia ； multiple impacted supernumerary teeth

並列摘要

鎖骨顱骨發育不良為罕見之自體顯性遺傳疾病，發生率約為百萬分之一。此疾病因控制成骨細胞特殊轉錄因子發生基因突變，使骨骼及軟骨的發育異常，影響顱骨、顏面骨及鎖骨。口腔方面的臨床特徵，常見有恆齒齒列延遲或異位萌發、多發性贅生齒、乳牙齒列牙根的延遲吸收、恆齒及贅生齒之牙根彎曲，及合併有明顯的咬合關係不良。本病例報告為一位二十八歲女性，患者來診時，口內僅萌發十一顆恆齒，十四顆乳齒未脫落，而上下顎骨中有二十一顆阻生恆齒及十八顆阻生贅生齒。病患呈現安格氏第三級咬合不正，至本院齒顎矯正科門診進行評估治療，後轉介至口腔顎面外科進行阻生贅生齒拔除及阻生恆齒手術暴露，同次進行矯正裝置置入及阻生恆齒強逼萌出。

並列關鍵字

鎖骨顱骨發育不良 ； 多發性阻生贅生齒