摘要
小淋巴管擴張症是一種由於小腸壁的淋巴管異常擴張，導致過量的蛋白質自腸道流失，而造成低蛋白症及水腫現象的一種疾病。臨床上，此病多好發於兒童及年青成人。百分比之九十的患者年齡小於三十歲，其中約有四分之三的病例是散在性病患。由組織學觀察，此種疾病的小腸黏膜層及黏膜下層有典型之琳巴管擴張。患者的主要症狀是水腫，有時併有脂肪下痢。診斷此症可由小腸之切片病理檢查，或是以標有放射性活動性巨分子之蛋白質證明蛋白質自腸道流失。亦可測阿爾發一1一抗胰蛋白酶之小腸廊清率獲得證實。本篇報告一例二十三歲女病例，主訴水腫。血液生化檢驗發現血清蛋白僅1.5g／de，經小腸切片檢查後，診斷為小腸淋巴管擴張症。
關鍵字
小腸淋巴管擴張並列摘要
Intestial lymphangiectasia is a disease chraacterized by dilated intesinal lymphatic channels. Hypopro-tinemia and edema resulted from increased enteric loss protein. This disease affects primarily in children and young adults. More than 90% of the patient’s age is under 30 years old about third- fourth of the cases is sporadic. The histological abnormality is dilatation of the lymph vessels of the small intestinal mucosa and submucosa. The major symptom is edema, and steatorrhea occasionally. The diagnosis is established by small intestinal biopsy or demonstration of enteric protein loss using redioactine macromolecule, or alpha-l-antitryp-sin clearance. We reported a female patient of twenty-three years old with the chief complaint of edema.biochemistry examination revealed the serum albumin was 1.5 g／dl, small intestinal lymphangiectasia was diagnosed after small intestinal biopsy.