Primitive Neuroectodermal Tumor of the Kidney: A Case Report and Literature Review

腎臟原始神經外胚層腫瘤：病例報告與文獻回顧

蔡佩珊(Pei-Shan Tsai) ； 黃彥霖(Yen-Lin Huang) ； 楊斐適(Fei-Shih Yang)

《中華放射線醫學雜誌》 35卷3期 (2010/09) Pp. 159-163

摘要

原始神經外胚層腫瘤是一種罕見的惡性肉瘤，大多數來自中樞神經系統。發源於身體周邊並不常見，而源自於腎臟的原始神經外胚層腫瘤更是少之又少。大多數文獻指出，原發性的腎臟原始神經外胚層腫瘤多發生於小孩或年輕人身上。我們報告了一位40歲男性病患，因右腰部無痛腫塊來求診，影像上顯示一個巨大的右腎腫瘤，注射顯影劑後，腫瘤呈現不均勻的顯影，並夾有壞死及出血。最終開刀後的病理結果為罕見的腎臟原始神經外胚層腫瘤。文中將描述影像上的發現並作相關文獻的回顧。

並列摘要

Primitive neuroectodermal tumors (PNET) are sarcomas that arise most commonly in the central nervous system. The much less common peripheral PNETs have been reported in many body sites, but renal PNET is extremely rare. Most renal PNETs occur in children or adolescents. We report a 40-year-old man presenting with an enlarging right flank mass for one month. Computed tomography (CT) demonstrated a large exophytic soft tissue mass with heterogeneous enhancement originating from the right kidney and containing areas of necrosis and hemorrhage. The tumor was completely resected, and the pathological examination revealed a renal PNET. The imaging findings of this tumor were discussed, and the literatures were reviewed.