- 期刊
- OpenAccess
Fuchs'角膜內皮細胞失養症－二家族病例報告
Fuchs' Endothelial Dystrophy-Two Family Cases Report
摘要
Fuchs'角膜內皮細胞失養症是東方人較罕見的家族性角膜疾病，國內尚無家族病例報告。本文報告兩家族共三例有第二級以上之內皮滴狀變化，其中有一例並有明顯之角膜水腫，並追踪其家族成員之內皮細胞變化，其中二例屬同一家族，其他成員內皮正常；第三例其家族中另有三人有第一級內皮滴狀變化。此變化之臨床意義則尚待進一步探討。
關鍵字
無資料並列摘要
Fuchs' endothelial dystrophy is a hereditary bilateral corneal degeneration manifested as the development of cornea guttata at endothelial layer in the middle age which progresses to corneal edema in the later stage. This disease is especially rare in our population. We report the clinical findings of 3 cases from 2 families who have Fuchs' endothelial dystrophy. Also the clinical finings and corneal endothelial morphology of the other members of these families are presented. Two of the 3 cases belongs to one family. The other members of these family are essentially normal in their ocular examination and endothelial morphology. While The 3rd case has 3 relatives presented with grade 1 corneal guttata. The clinical significance of This finding demands further investigation.
延伸閱讀
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