We reported a 28-year-old female patient with no systemic illness who presented with chronic intermittent hemoptysis for 5 years. Chest computed tomography revealed pulmonary sequestration with 1 feeding artery originating from the celiac trunk. Right lower lung lobectomy with pulmonary sequestration resection was performed, after which, the hemoptysis resolved. By presenting this case we hope to emphasize the concept that pulmonary sequestration cannot be excluded by a normal chest x-ray, and that pulmonary sequestration alone can be the cause of chronic intermittent hemoptysis in an otherwise asymptomatic patient. A review of the literature on pulmonary sequestration is also presented.