Unusual Radiographic Manifestation of Organizing Pneumonia in a Patient with Sjogren’s Syndrome

修格連氏症候群是自體免疫疾病，往往會影響身體不同器官。在肺部的表現，通常包含支氣管炎，支氣管擴張，或是間質性肺炎。在間質性肺炎中，以非特異性間質性肺炎（nonspecific interstitial pneumonia）、淋巴細胞間質性肺炎（lymphoid interstitial pneumonia）及器質性肺炎（organizing pneumonia）最常出現。在本病例報告中，個案因修格連氏症候群合併器質性肺炎，在影像學上的表現，與大多數器質性肺炎靠近肋膜處實質化（pleura-based consolidation）較為不同，而是以兩側多處結節性型態為主。器質性肺炎最終以胸腔內視鏡輔助手術切片輔助診斷。器質性肺炎在自體免疫疾病中表現有非常大的差異性，因此我們必須更積極取得好的病理組織切片，及早確診並及時施以類固醇，讓病患接受有效治療是相當重要的。

關鍵字

器質性肺炎；修格連氏症候群；間質性肺炎；肺結節；胸腔內視鏡輔助手術

並列摘要

Sjogren’s syndrome is an autoimmune disease that can affect exocrine organs and many different parts of the body, including the lungs. The usual pulmonary manifestations of Sjogren’s syndrome include bronchiolitis, bronchiectasis and interstitial pneumonias. In Sjogren’s syndrome-associated interstitial pneumonias, the common patterns are nonspecific interstitial pneumonia, lymphocytic interstitial pneumonia, and organizing pneumonia. Here, we report a case of Sjogren’s syndrome with organizing pneumonia. The radiographic presentation of this case was multiple nodules rather than the typical pattern of organizing pneumonia, which usually presents pleura-based consolidation. The diagnosis of organizing pneumonia in this case was made by video-assisted thoracoscopic biopsy. Particular issues regarding radiographic features and diagnostic approach in this case were addressed in this report.

並列關鍵字

organizing pneumonia ； Sjogren's syndrome ； interstitial lung disease ； lung nodule ； videoassisted thoracoscopy

國際替代計量

Unusual Radiographic Manifestation of Organizing Pneumonia in a Patient with Sjogren’s Syndrome

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