Expandable Congenital Lung Cysts: A Case Report

可擴張之先天性肺囊腫：一病例報告

李淑婷(Shu-Ting Lee) ； 林隆煌(Lung-Huang Lin) ； 陳五常(Wu-Charng Chen) ； 那明珠(Minkyu Nar)

《輔仁醫學期刊》 4卷2期 (2006/06) Pp. 107-112

摘要

先天囊腫性肺部疾病為一系列相關的先天性異常，其中包括先天性肺氣腫，支氣管囊腫，先天囊腫性腺瘤樣畸形及游離肺。其中先天囊腫性腺瘤樣畸形目前被認為是肺間質在妊娠5到7週時無法成功的誘發部分胎兒支氣管肺泡的分化所致。我們報告一例男性新生兒在出生後出現呼吸困難，壓力性氣胸，及愈來愈大的肺部囊腫，其臨床診斷為先天囊腫性腺瘤樣畸形。在本文中我們敘述此病例的臨床及影像學上的表現，以及首次在此疾病中敘述可擴大的肺部囊腫。

關鍵字

先天囊腫性腺瘤樣畸形 ； 先天囊腫性肺部疾病 ； 先天性肺囊腫

並列摘要

Congenital cystic lung diseases comprise a spectrum of interrelated abnormalities that include congenital lobar emphysema (CLE), bronchogenic cysts, congenital cystic adenomatoid malformation (CCAM), and pulmonary sequestration. CCAM is thought to result from a failure of the pulmonary mesenchyme to induce normal bronchoalveolar differentiation in a part of the fetal lung between the fifth and seventh weeks of gestation. We describe a male newborn who presented with respiratory distress, tension pneumothorax, and expanding lung cysts after delivery; he was clinically diagnosed as having CCAM. We are the first to describe the clinical and image presentations of expandable lung cysts under ventilation.

並列關鍵字

congenital cystic adenomatoid malformation ； congenital cystic lung disease ； congenital lung cyst