Huge Chest Wall and Intrathoracic Desmoid Tumor: A Case Report and Literature Review

Lai-Man Mok ； Yu-Chao Yu ； Mei-Lin Chan ； Wen-Chien Huang

《胸腔醫學》 37卷1期 (2022/03) Pp. 27-32

摘要

A desmoid tumor of the chest wall is rare. It is a slow-growing soft-tissue tumor, but also has an infiltrative growth tendency, which leads to a higher risk of local recurrence. However, it seldom metastasizes due to its benign nature. Surgical excision is the mainstay of treatment for the disease. Chest wall reconstruction would be necessary when a huge defect or loss of stability result from resection. Thus, a large tumor size and some specific locations would increase surgical complexity, which might lead to morbidity and mortality. We reported a 52-year-old female with a huge intrathoracic tumor. The patient underwent surgery for tumor removal via a sternotomy. The wound was extended to the left lower neck since the tumor was located at the left apex and close to the great vessels. Final pathology proved the diagnosis of a desmoid tumor of the chest wall and thoracic cavity. We presented the clinical features of the desmoid tumor and a discussion on management options and considerations.

關鍵字

desmoid tumor ； fibromatosis ； intrathoracic tumor ； chest wall tumor ； surgical treatment