- 期刊
A Non-Syndromic Case of Syndactyly Hands Associated with Dental Abnormality: A Case Report
非症候群之雙手併指合併牙齒異常：病例報告
摘要
Syndactyly combined with dental abnormality often can be associated with craniofacial syndromes, such as Apert syndrome, oclulodentaldigital dysplasia. It's difficult to diagnose rare non-syndromic cases due to varied presentation of multiple dental abnormalities. A 3yr4m old girl who has scaphocephaly, retrognathism profile, flattened nose, narrow palate, lip incompetence, mouth opening limitation, teeth hypoplasia and syndactyly of hands with full mouth multiple dental caries, showed unstable behavior during series of dental treatments. Full mouth rehabilitation was completed with multiple behavior management skills (positive reinforcement, distraction and isolation) in 6 appointments. It is challenging to make correct diagnosis and to make an aggressive, proper dental treatment plan when facing these high caries risk and unstable behavioral patients.
並列摘要
併指合併牙齒發育異常時常是基因變異引起之多種先天症候群的症狀之一，如亞伯氏症、眼齒指發育不全等。此病例為一名三歲四個月女孩，外型為舟狀頭、下顎後縮、鼻塌陷、上顎狹窄、嘴唇無法輕鬆閉合以及雙手併指經外科手術分指。口內症狀包含牙齒牙釉質發育不良、張口困難以及全口嚴重早發性齲齒。病患於牙科門診搭配行為引導（正向強化、分散注意力以及隔離家長）完成全口重建，維持定期回診及塗氟。對於牙醫師而言，面對此類蛀牙風險高且治療配合度較低之病患困難度除了正確的牙科診斷、積極與完善的牙科照護計畫，亦須依照其他臨床症狀判斷是否需要適時轉介，以利提供病患多方面適當的評估與治療。
延伸閱讀
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