牙本質形成不全 ─ 病例報告

Dentinogenesis Imperfecta : Report of Two Cases

項文宣(Wen-Hsuan Hsiang) ； 張家豪(Chia-Hoa Chang)

《中華民國兒童牙科醫學會雜誌》 2卷3期 (2002/10) Pp. 76-83

https://doi.org/10.6319/JTAPD.2002.2(3).6

摘要

牙本質形成不全(Dentinogenesis imperfecta, DI)，為一種自體顯性遺傳疾病，有時會有骨發生不全(Osteogenesis imperfecta, OI)，伴隨發生。牙齒呈現褐色、透明、易脆等特徵。當牙齒萌發時，家長發現其問題，而會尋求兒童牙科醫師的建議、治療。本篇文章藉由臨床所見之牙本質形成不全第一類型及第二類型(DI type I 、DI type II)的病例報告，討論治療的目的、方法。咸信早期診斷、治療，及定期追蹤檢查，可預防牙齒損壞，適時遏止咬合的惡化，並改善美觀，恢復患者的自信心。

關鍵字

牙本質形成不全 ； 骨發生不全 ； 牙本質

並列摘要

Dentinogenesis imperfecta (DI), in which the teeth are discolored, translucent and brittle, can occur in isolation as a familial trait and as a component of the skeletal dysplasia osteogenesis imperfecta (OI). As soon as the teeth erupt, the parents may notice the problem and look for a pediatric dentist's advice and treatment. The purpose of this article is to present the objects, treatment options, and problems encountered in the treatment of Dl through the two cases including DI type I and type II. Early diagnosis, treatment and long term follow-up are recommended, as it may prevent or intercept deterioration of the teeth and occlusion and improve esthetics.

並列關鍵字

Dentinogenesis Imperfecta ； Osteogenesis Imperfecta ； Dentin