Hepatopulmonary Syndrome: Report of One Case

肝肺症候群：一病例報告

葉政南(Cheng-Nan Yeh) ； 王玠能(Jieh-Neng Wang) ； 楊燿榮(Yao-Jong Yang) ； 吳俊明(Jing-Ming Wu) ； 姚志達(Chi-Ta Yao)

《Acta Paediatrica Taiwanica》 46卷4期 (2005/08) Pp. 222-225

https://doi.org/10.7097/APT.200508.0222

摘要

肝肺症候群，其臨床上診斷的條件包括：慢性肝病變，低血氧症及非心因性或肺部疾病所引起之肺內血管擴張。根據文獻報告，此併發症在慢性肝病變患者並不罕見（發生率約4-29%），但常由於臨床表現並不嚴重而被忽略，因而沒有早期發現。我們報告一位十九歲女性，其在出生時便因先天膽道閉鎖不全接受手術治療，之後出現慢性肝硬化以及低血氧症狀，經顯影性心臟超音波(contrast echocardiography)、心導管檢查、及(上標 99m)Tc肺部灌流掃描，證實為肝肺症候群。本文目的在提醒臨床醫師，若在慢性肝病變患者出現低血氧症狀，則必須將此疾病列入鑑別診斷。

關鍵字

肝肺症候群 ； 低血氧症 ； 肝硬化

並列摘要

Hepatopulmonary syndrome consists of a triad of chronic liver disease, hypoxemia, and intrapulmonary vascular dilatation in the absence of primary cardiac or pulmonary diseases. Though this complication has been described in as many as 4-29% of patients with liver disease, its clinical manifestations are often subclinical. The standard diagnostic tests for hepatopulmonary syndrome are the applications of contrast echocardiography and (superscript 99m)Tc lung perfusion scan. In this report, we describe a 19-year-old female with biliary atresia and subsequent liver cirrhosis, who also had the complication of hepatopulmonary syndrome since adolescence. We conclude when the symptoms and signs of hypoxemia appear in a patient with chronic liver disease, the differential diagnosis of hepatopulmonary syndrome should be kept in mind.

並列關鍵字

hepatopulmonary syndrome ； hypoxemia ； liver cirrhosis