Image on Clinical Medicine: Capillary Telangiectasia in Juvenile Dermatomyositis

Translated Titles





陳士哲(Shi-Zhe Chen);吳建璋(Chien-Chang Wu);郭建宏(Chien-Hung Kuo);黃素雲(Su-Yun Huang);彭洸萍(Guang-Ping Peng);高佳慧(Jia-Hui Kao);段彭年(Pong- Nien Tuan)

Key Words

juvenile dermatomyositis ; periungual telangiectasias ; poikiloderma ; 青少年型皮肌炎 ; 甲周血管擴張症 ; 多形性皮炎



Volume or Term/Year and Month of Publication

13卷2期(2019 / 12 / 01)

Page #

116 - 118

Content Language


Chinese Abstract

Juvenile dermatomyositis (JDM) is the early-onset form of dermatomyositis, a systemic, autoimmune inflammatory muscle disorder characterized by proximal muscle weakness, characteristic skin lesions, and systemic manifestations. The course of JDM is highly variable: Some patients go into remission within 2-3 years, whereas others followed a cyclic course marked by relapses. The aim of treatment is to reduce long-term morbidity and restore physical function. High-dose corticosteroids are the mainstay of treatment, and dose tapering after a few weeks of therapy depends on the patient response. In this imaging report, we present the case of a 10-year-old girl diagnosed with JDM based on the classical findings of heliotrope rash, Gottron's papules, poikilodermatomyositis, elevated skeletal muscle enzyme levels, bilateral proximal muscle weakness, and denervation myopathy of the left rectus femoris and biceps muscles. Additionally, periungual erythema and telangiectases, filamentous or spider-like capillary changes were observed on bilateral hands by nailfold capillaroscopy.

English Abstract


Topic Category 醫藥衛生 > 醫藥衛生綜合