摘要
IgG4相關性疾病是這十年來一種新的多重器官影響、多重系統性表現的疾病，此疾病常見特徵為IgG4血清濃度大於135mg/dl、受侵犯組織有大量IgG4陽性漿細胞浸潤、席紋樣纖維化（storiform fibrosis）、閉塞性靜脈炎（obliterative phlebitis）。診斷主要由臨床表現以及組織切片的病理結果。治療主要是使用皮質性類固醇以及免疫抑制劑，對於治療反應不佳的患者可以考慮採用抗B細胞治療。
參考文獻
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