中耳內的顏面神經先天性異常在中耳手術中是少見的,主要可分為骨性裂開(bony dehiscence)、解剖位置及神經路徑走向變異、鼓索神經解剖變異以及持續存在的胚胎期血管;而其中顏面神經經由卵圓窗下方走向的病例更是少見。先天性顏面神經異常最常發生於顏面神經的鼓室段,大多與顳骨或聽小骨的先天異常併存,且主要原因是胚胎時期第一及第二鰓弓的發育異常所造成。本科於1993年5月間經歷一病例,主訴為右耳聽障併耳鳴30年,檢查後在懷疑右側耳硬化症下進行中耳探測手術,術中發現顏面神經的鼓室段有骨性裂開且走在卵圓窗(oval window)下方,同時併有鐙骨(stapes)的異常。在此提出報告以供參考,由於中耳顏面神經異常經常與顳骨或聽小骨的先天異常併存,於手術中必須特別小心避免傷及顏面神經。
We present a case of 41-year-old man, who had unilateral hearing impairment since childhood and received exploration of the middle ear under the suspicion of otosclerosis. The facial nerve was found to have an anomalous course inferior to the oval window. A deformed stapes was present as well. Extreme care of the facial nerve is advised in exploration for correcting middle ear anomaly.