左位心症候羣，雙主動脈弓合併血管環之一病例

A Case of Isolated Levocardia and Double Aortic Arch with Vascular Ring

蕭正貴(Cheng-Quei Shaio) ； 黃碧桃(Be-Tau Hwang) ； 孟春昌(C. C. Laura Meng)

《Acta Paediatrica Sinica》 21卷4期 (1980/12) Pp. 276-281

摘要

本報告病例，爲30天大之男嬰，出生後家人即發現呼吸時有噪雜聲音，但無呼吸及吞嚥困難現象。至15天大時，被發現有心雜音，所以至本院作進一步檢查及治療。經檢查證實爲左位心，腹部臟器轉位及雙方脈弓合併血管環，因爲罕見，故提出報告。

並列摘要

Isolated levocardia with vascular ring is a congenital disorder. The incidence in cardiovascular cases operated was reported as 1.4%. These patients usually died in early infancy unless early diagnosis and optimal treatment were made.
A male infant was born to a 30-year-old woman after full term pregnancy and normal spontaneous delivery. The birth weight was 3,400gm. Physical examination revealed noisy breathing and subcostal retraction. A Grade Ⅱ/Ⅵ systolic ejection murmur was heard over the 2nd-3rd ICS along left sternal border. Chest X-ray films demonstrated slight cardiomegaly and normal pulmonary vascularity. The liver shadow was at the left side. EKG showed right axis deviation of the QRS mean axis with an upright P wave in aVR and inverted P wave over lead I. Echocardiograms showed aorta and pulmonary artery simultaneously with anteriorly located aorta and posteriorly located pulmonary artery. The esophagogram showed double aortic indentation at the upper portion of the esophagus and a right- sided stomach.
Cardiac catheterization and angiocardiography demonstrated isolated levocardia, atrial inversion, D-transposition of the great vessels, interatrial septal defect, interventricular septal defect, pulmonary stenosis and a double aortic arch forming a vascular ring.

並列關鍵字

levocardia ； vascular ring ； situs inversus