- 期刊
Romano-Ward症候羣之一病例報告
Romano-Ward Syndrome: Report of a Case
摘要
本文報告一名14歲女孩，因多次暈厥及抽搐發作，由心電圖得知爲心室頻脈及心室摸動所致。不整脈以propranolo控制後發現QT間隔顯著延長，因其聽力正常故診斷爲Romano-Ward症候羣。本例發作之誘因爲月經亦可能與聽覺刺激有關；家族中無類似發作，然其母親及外祖母之QTc延長，雖然有遺傳因存在。本例與文獻記載不同的是運動反使心室不整脈得到緩解，而非誘因；作者相信是因爲運動時QTc縮短的緣故。本例以propranolol治療，效果極佳。
關鍵字
無資料並列摘要
Reported is a case of Romano-Ward syndrome in a 14-year-old Taiwanese girl, manifested by syncope and convulsion secondary to ventricular tachydysrhythmias, Q-T prolongation in electrocardiograms, and normal hearing. Extensive studies excluded the possibilities of any organic heart disease or Q-T prolongation secondary to other causes. Family study revealed slight prolongation of QTc in the mother and maternal grandmother, both of whom were asymptomatic. Propranolol effectively prevented recurrence of ventricular tachydysrhythmias; each recurrent episode of syncope was associated with menstrual cycle, auditory stimulation, and discontinuation of medication. This is, to the best of our know-ledge, the first reported case of Romano-Ward syndrome in pediatric age group in Taiwan.
延伸閱讀
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