Kawasaki Disease Presenting with Disseminated Intravascular Coagulation: Report of One Case

以全身性血管內凝血病及血小板過低症表現的川崎氏症：－病例報告

黃麗薇(Lei-Wei Huang) ； 孫武(Wu Sun) ； 黃富源(Fu-Yuan Huang)

《Acta Paediatrica Sinica》 35卷4期 (1994/08) Pp. 341-344

https://doi.org/10.7097/APS.199408.0341

摘要

川崎氏症的血液相變化，經常包括貧血、白血球增加、以及血小板增加。然而以血小板過低來表現的川崎氏症，卻相當罕見。本篇報告一例3月女嬰，在臨床上表現典型的川崎氏症特征，卻出現血小板減少及全身性血管內凝血的變化。此病患在發病第三天到本院求診，在發病第四天接受免疫球蛋白的治療，並在發病第十天有血小板增加的變化。因此我們開始給予低劑量阿斯匹靈(adpirin)，並且持續治療三個月。在往後的八個月追蹤過程中，此女嬰的健康情形良好，同時心臓超間波檢查也顯示正常。

關鍵字

川崎症 ； 血小板減少 ； 瀰漫性血管內凝血

並列摘要

Thrombocytosis is always noted in patients with Kawasaki disease (KD). Here we present a case of KD with an unusual finding of thrombocytopenia.
A 3 months old female baby was admitted to our hospital presenting with the classical symptoms and signs of KD. However, initially she also had thrombocytopenia and disseminated intravascular coagulation. She was treated successfully with a single high dose of intravenous immunoglobulin. (2gm/kg). Thrombocytosis was found on the 10th day of illness, and treatment with low dose aspirin was administered for 3 months. No coronary aneurysm was found on cardiac echography. She was found to be well on a follow-up of 8 months.

並列關鍵字

Kawasaki disease ； thrombocytopenia ； disseminated intravascular coagulation