- 期刊
Flow Characteristics in Infants with Hypoplastic Left Heart Syndrome: An Echocardiographic Study
嬰幼兒左心發育不全症候群超音波心圖的血流特徵
摘要
自從一九九二年七月至一九九三年一月，有五例左心發育不全症候群（以下稱本病），經由超音波心圖診斷，并有一例由心導管，二例由手術證實。 由於本病的預後不佳，且血流動力變化不穩定，因此我們著手於研究其超音波心圖的血流動力特徵。結果發現：在收縮期時，在升、降主動脈是順向（前進）血流，在橫主動脈是逆向血流，在動脈導管是右至左分流。在舒張期時，其血流方向正好反向而流。另外升主動脈的“舒張期逆向血流”，幾乎是本病的另一特徵，可由以鑑別診斷。超音波心圖除了是項有力診斷利器之外，本病在超音波心圖上的血流特徵，還可以幫助我們了解其血流動力及疾病生理學。
並列摘要
From July 1992 to January 1993, a total of 5 cases of hypoplastic left heart syndrome were diagnosed by echocardiograms and confirmed by available angiographic, surgical or autopsy results. The flow dynamics disclosed by spectrum display in the aortic root and patent ductus arteriosus (PDA), in systole, were: (1) antegrade in the ascending aorta and descending aorta (below PDA), and retrograde in the transverse aorta, and (2) right-to-left shunt in the FDA. While in diastole, there were (1) antegrade in the transverse aorta, and retrograde in the ascending aorta and descending aorta (below FDA), and (2) left-to-right shunt in the FDA. No ventriculocoronary fistulas were identified. With both the characteristic flow pattern and the extremely narrow diameters of the ascending aorta in hypoplastic left heart syndrome, we can differentiate it from those heart diseases associated with secondary hypoplastic left heart due to total anomalous pulmonary venous connection or congenital pulmonary venous stenosis. Both help us understand better the hemodynamics and pathophysiology of hypoplastic left heart syndrome in these patients.
延伸閱讀
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