第三腦室未成熟畸胎瘤在臨床上是極為少見的病例,通常此類的病人往往表現出水腦或是顱內腫瘤引發之顱內壓升高等等症狀。我們提出一十個月大的女嬰,出現有嚴重的頭痛、嘔吐等顱內壓升高的問題,在核磁共振檢驗之下,發現有第三腦室腫瘤合併有水腦的問題,因此緊急採取手術摘除腫瘤及減壓,術後病人症狀得到了顯著的改善。我們將回溯文獻有關於未成熟畸胎瘤的臨床症狀、手術治療及預後,並討論手術、放射治療和其預後的關聯。
We present the case of a 1-year-old girl with persistent vomiting who was found to have a disproportionately large immature teratoma in the third ventricle. Magnetic resonance imaging demonstrated a heterogeneous intracranial mass in the third ventricle, with a compressed left cerebral hemisphere and hydrocephalus. Bifrontal craniotomy via a transchiasmatic approach achieved total resection of the tumor. No significant neurologic deficit was seen except for double vision and disturbances in eye movement. Third ventricle immature teratoma, although extremely rare, may present as a suprasellar mass lesion and hydrocephalus. The prognosis after gross total resection is favorable; however, radiotherapy is usually postponed until 36 to 48 months of age in order to avoid complications such as stunted growth, endocrine disturbances and neuropsychologic problems.