Primary Cardiac Angiosarcoma Presenting with Pericardial Effusion and Cardiogenic Shock – Two Cases Report

原發性心臟腫瘤的發生率大約為0.001%至0.28%，在惡性腫瘤中又以肉瘤佔大多數，其中以血管肉瘤最常見。此腫瘤最常發生在右心房內，常會侵延至心包膜，靜脈腔、或三尖瓣，而引至心包填塞或心內血流阻礙。我們報告兩例血管肉瘤，因其合併大量心包滲液及在三尖瓣處的血流阻礙，而引致心因性休克，雖經切除原發性腫瘤，但仍有一例因心房竇功能不良及心律過慢而常要放置永久心律起動器，而另一例則有復發性之腫瘤合併部轉移。現雖能以非侵犯性的技術發現腫瘤及積極給予切除，但亦只能存活數月，目前仍未有好的治療方法。

關鍵字

血管肉瘤；心包積水；心因性休克

並列摘要

Primary tumors of the heart occur with an incidence rate of 0.001% to 0.28%. Sarcomas comprise the largest proportion of primary malignant cardiac tumors. Angiosarcoma is the most common malignant tumor of the heart. This tumor is found most often in the right atrium and frequently extends to the pericardium, vena cava, or tricuspid valve, causing tamponade and/or heart inflow obstruction. We present 2 cases of angiosarcoma with cardiogenic shock due to massive pericardial effusion and obstruction to blood flow in the tricuspid valve area. After having resection of the original tumors, l patient needed to have pacemaker implantation due to sinus node dysfunction with junctional bradycardia, while the other patient had recurrent cardiac tumor and lung metastases. Despite diagnosis by noninvasive imaging procedures and aggressive early surgical intervention, survival in both cases was less than few months. Thus, optimal therapy is unclear.

並列關鍵字

angiosarcoma ； cardiogenic shock ； pericardial effusion

國際替代計量

Primary Cardiac Angiosarcoma Presenting with Pericardial Effusion and Cardiogenic Shock – Two Cases Report

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