Apical Hypertrophic Cardiomyopathy: The Ace-of-Spades as the Disease Card

Cornelia C. Diaconu ； Nicoleta Dumitru ； Ana G. Fruntelata ； Smarandita Lacau ； Daniela Bartos

《Acta Cardiologica Sinica》 31卷1期 (2015/01) Pp. 83-86

https://doi.org/10.6515/ACS20140310C

並列摘要

Apical cardiac hypertrophy (Yamaguchi syndrome) is a relatively rare form of hypertrophic cardiomyopathy. A 67-year-old woman presented with exertional angina and moderate dyspnea. Her electrocardiogram showed sinus rhythm, flattened T waves in the limb leads and a strain pattern in the V_2-V_6 Ieads. Echocardiographic examination showed that apical wall thickness of the left ventricle (LV) was 19 mm. Coronary angiography was normal, but left ventriculography revealed a spade-like shaped LV cavity, typical for apical cardiac hypertrophy. The diagnostic criteria for apical cardiac hypertrophy are: 1) asymmetric LV hypertrophy - predominantly at the apex of the ventricle; 2) LV wall thickness of 15 mm or more during diastole; and 3) apical to posterior wall thickness ratio of 1.5 or more determined by 2-dimensional echocardiography or cardiac magnetic resonance imaging. Although relatively rare, Yamaguchi syndrome must enter into the differential diagnosis of patients presenting with exertional angina pectoris.

並列關鍵字

Angina pectoris ； Hypertrophic cardiomyopathy