Primary carcinoma of choroid plexus are rare and found most frequently in children than in adults. In children, the choroid plexus carcinoma are located predominantly in the lateral ventricles, while adults in the fourth ventricle. This report is about a 53 year old male with primary carcinoma located in the lateral ventricle with CSF metastases, which was treated with total tumor excision of choroids plexus followed by post-operative cranial spinal irradiation. This paper aims at the possibilities and limitations of the treatment of primary carcinoma of choroids plexus.