Urachal adenocarcinoma is an extremely rare neoplasm and usually associated with poor prognosis. We report a case of urachal adenocarcinoma in one 44-year-old woman. She presented painless hematuria. Cystoscopic examination and transurethral biopsy showed an urachal tumor. After undergoing laparoscopic partial cystectomy with lymph nodes dissection, the patient received postoperative radiation therapy. The clinical presentation, radiological, histopathological findings, treatment methods and correlated literature are discussed and reviewed here.