Congenital rib absence is an uncommon anatomic anomaly. This lesion has been reported in fetuses, newborns, infants and small children, but it is very rare in adults. A 42-year-old male patient presented to our clinic due to blunt chest trauma. He complained of chest pain on the left chest due to trauma. Chest computed tomography revealed the fullness of the chest, but the anterior part of the 1^(st)rib was missing, and left 6^(th)-9^(th) rib fractures were noted. The three-dimensional reconstruction of the computed tomography showed left 6^(th)-9(th) rib fractures, absence of the anterior part of the 1^(st) rib, the manubrium sterni tilted to the lower right, and a pair of lumbar ribs. He was advised to rest and have regular follow-up. Asymptomatic patients with missing ribs usually do not require management. Surgical treatments are only indicated for patients missing ribs with severe symptoms or a severely deformed ribcage. Lumbar ribs are usually also asymptomatic and do not have any important clinical significance. An early diagnosis of lumbar ribs is necessary for avoiding misguidance in the surgical locations. This is the first case report of a congenital rib absence combined with lumbar ribs.