Solid Cystic Pseudopapillary Tumor of the Pancreas: Report of One Case

胰髒之假乳頭狀固形囊腫：一病例報告

蘇玄白(Hean-Pat Saw) ； 何茂霖(Mao-Lin Ho) ； 陳家玉(Jia-Yuh Chen)

《Acta Paediatrica Taiwanica》 44卷6期 (2003/12) Pp. 368-371

https://doi.org/10.7097/APT.200312.0368

摘要

胰髒之假乳頭狀固形囊腫之病例在兒童非常罕見。在此我們的出一位十二歲女童，在疾病早期並無任何症狀，直到腫瘤變大而壓迫到附近的器官之後才出現症狀。此病患的臨床表徵爲腹部間接痙攀性腹部疼痛、嘔吐、排便習慣改變以及食慾變差。此腫瘤是利用腹部超音波、電腦斷層或核磁共振作爲手術前的診斷。在此病患腹部電腦斷層的右上方發現有一個大的腫塊。由於腫塊非常接近胰髒頭部，而且在手術當時懷疑有附近組織擴散，因此病患接受了胰髒十二指腸手術。確實的診斷主要是靠病理組織所見。在肉眼下，包含有包被合併有囊腫遍性以及出血性壞死。在顯微鏡下，它有顯著的乳頭狀排列混合固形區域。這種腫瘤在接受完全切除手術後會有很好的預後。此患者經過我們一年多來的追蹤，到目前爲止並沒有複變以及發生任何併發症。由於此腫瘤有複發的可能性，因此建議必須做追蹤。

關鍵字

胰髒豭乳頭狀腫瘤 ； Frantz's腫瘤

並列摘要

Solid cystic pseudopapillary tumors of the pancreas (Frantz’s tumor) are rare in children. We present a 12-year-old child with a pancreatic tumor without initial symptoms or signs until the tumor compressed the adjacent organs. The child had clinical presentation of intermittent abdominal cramping pain, vomiting, changes in bowel habits and decreased of appetite for 2 days. The abdominal computed tomography showed a mass that measuring 6×7×7cm at the right upper quadrate. Whipple operations with pylorus-preserved pancreato-duodenectomy and cholecystectomy were performed. The definite diagnosis was made by the post-operation pathological finding. Grossly, the tumor was encapsulated with cystic degeneration and hemorrhagic necrosis appearance. Microscopically, it had predominantly papillary arrangement mixed with solid areas. Prognosis of this tumor was good under complete resection. The patient remained well with no signs of recurrence or malignant changes at 1 year after operation. Due to the possibility of recurrence, close follow up is recommended.

並列關鍵字

pseudopapilary tumor of pancreas ； Frantz's tumor