Dental Consideration for the Treatment of Patient with Prader-Willi Syndrome - A Case Report

普瑞德威利症候群患者的牙科治療考量－病例報告

劉仕元(Shih-Yuan Liu) ； 孫國丁(Kuo-Ting Sun)

《臺灣兒童牙醫學雜誌》 20卷4期 (2020/12) Pp. 153-157

https://doi.org/10.6319/TJPD.202012_20(4).0004

摘要

Prader-Willi syndrome (PWS) is a genetic disorder which occurs with a frequency about one in 10,000-30,000 live newborns. Both males and females, and all races are equally effected. The numerous symptoms of PWS include the following: delay development, hyperphagia and obesity, changes in the salivary composition and consistency, enamel erosion, severe tooth wear, etc. This article presents a case of 3-year-old boy with PWS. Due to his multiple caries and behavior problem, the dental treatment was finished under general anesthesia. PWS involved many aspects, the early diagnosis and treatment are essential to improve the general health and the quality of the life for these individuals.

關鍵字

Prader-Willi syndrome ； Dental treatment ； General anesthesia

並列摘要

普瑞德威利症候群（又稱小胖威利症）是一種遺傳性疾病，新生兒的發生率約為1/10,000～1/30,000。男性和女性，以及不管任何人種的發生率皆相當。普瑞德威利症候群的症狀包括：發展遲緩、食慾亢進及肥胖、唾液的成分和稠度改變、牙釉質腐蝕、嚴重的牙齒磨耗等。本文案例為一個患有普瑞德威利症候群的三歲男孩，因為全口多處蛀牙及行為上的問題，整個牙科治療皆在全身麻醉下完成。普瑞德威利症候群會影響很多方面，早期的診斷及治療對於改善這些患者的全身健康及生活品質至關重要。

並列關鍵字

普瑞德威利症候群 ； 牙科治療 ； 全身麻醉