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嗜鉻細胞瘤和副神經節細胞瘤之心肌病變

摘要


嗜鉻細胞瘤(pheochromocytoma)和副神經節細胞瘤(paraganglioma)是分泌兒茶酚胺(catecholamines)的罕見神經內分泌腫瘤(neuroendocrine tumors)。典型的三症狀(classical triad)包含頭痛、盜汗以及心悸。另外可能會引起高血壓、低血壓、心因性休克(cardiogenic shock)、缺血性心臟病(ischemic heart disease)、心肌病變(cardiomyopathy)等症狀。手術將腫瘤切除為標準治療。經過手術將腫瘤切除後,約有96%的案例心肌病變會改善或是復原。左心室射出分率(left ventricular ejection fraction)會於手術後數週至一年內改善。

參考文獻


Zhang R, Gupta D, Albert SG. Albert b. Pheochromocytoma as a reversible cause of cardiomyopathy: Analysis and review of the literature. Int J Cardiol 2017;249:319-23.
Miura M, Kawano H, Yoshida T, et al. The Histological Features of a Myocardial Biopsy Specimen in a Patient in the Acute Phase of Reversible Catecholamine-induced Cardiomyopathy due to Pheochromocytoma. Intern Med 2017;56:665-71.
Ferreira AG, Nunes da Silva T, Alegria S, et al. Paraganglioma presenting as stress cardiomyopathy: case report and literature review. Endocrinol Diabetes Metab Case Rep 2019;2019:pii EDM190017.
Rostoff P, Nessler B, Pikul P, et al. Fulminant adrenergic myocarditis complicated by pulmonary edema, cardiogenic shock and cardiac arrest. Am J Emerg Med 2018;36:344.

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