Behçet's disease (BD) is a systemic vasculitis that commonly manifests itself in the form of mucocutaneous lesions, ocular and gastrointestinal involvements. It may also involve all organs such as the joints, central nervous system, and blood vessels of all types. The disease is uncommon in childhood, though it may occasionally present early onset before the age of 16 years. We report a rare juvenile Behçet's disease (JBD) and treatment course for the basis of further study.