Kimura Disease Occurred in Upper Arm of a 5-year-old Boy-A Case Report and Literature Review

發生於五歲男童上臂之木村病（Kimura disease）－一罕見個案報告與文獻回顧

莊昆霖(Kun-Lin Chuang) ； 謝式洲(Shyh-Jou Shieh) ； 邱浩遠(Haw-Yen Chiu)

《臺灣整形外科醫學會雜誌》 20卷4期 (2011/12) Pp. 330-338

https://doi.org/10.7096/TJTSPS.201112.0080

摘要

背景：木村病是一種罕見的慢性發炎性疾病，一般侵犯頭頸部的皮下組織與淋巴結。文獻上只有不到十例發生於上肢的病例報告。我們報告一例發生於上肢的木村病病例，據了解是目前最年輕的病例。目的及目標：報告一罕見病例，並針對此進行文獻回顧。材料及方法：病患為五歲男童，求診主訴為近六個月來左上臂漸漸變大的腫瘤。術前核磁共振檢查發現在遠端上臂尺神經旁有兩個腫瘤。手術除切除這兩個腫瘤外，在內前臂皮神經裡的一腫瘤病灶也一併切除。病理報告診斷為木村病。結果：病患於術後九個月的追蹤內沒有腫瘤復發的證據，而且保有良好的手部功能。結論：根據文獻，木村病沒有轉變為惡性的報告，但復發率高。發生在上肢的個案很少，治療方法包括手術切除，放射線治療與口服類固醇等。

並列摘要

Background:Kimura disease is a rare chronic inflammatory disorder involving the subcutaneous tissue and lymph nodes, typically of the head and neck area. Less than ten cases occurred on arms and hands were found from previous reports. In this report, we reported a patient suffered from Kimura disease affecting upper arm. To our knowledge, this is the youngest case in the literature.Aim and Objectives:To report a rare case and to review literatures on Kimura disease.Materials and Methods:A 5-year-old boy presented with a left upper arm enlarging soft tumor for six months. Preoperative MRI survey revealed two mass in distal upper arm adjacent to ulnar nerve.Surgical intervention was performed; the two masses and an additional lesion at the neighborhood of the medial antebrachial cutaneous nerve were excised. Pathology findings supported the diagnosis of Kimura disease.Results:The patient is free of recurrence at a 9-month follow up and has good hand function.Conclusion:Based on the literature review, Kimura disease bears no malignant potential, and with high recurrence rate. Involvement of the arms and hands is rare. Treatment of Kimura disease includes surgical excision, regional radiotherapy and systemic corticosteroid. (J Taiwan Soc of Plast Surg 2011; 20: 330∼338)

並列關鍵字

Kimura disease ； arm ； child