Kartagener氏症候群－病例報告

Kartagener's Syndrome - Case Report

顏宗弦(Tsung-Hsuan Yen) ； 胡克信(Ko-Hsin Hu)

《中華民國耳鼻喉科醫學會雜誌》 32卷5期 (1997/10) Pp. 450-454

https://doi.org/10.6286/1997.32.5.450

摘要

Kartagener氏症候群又稱為immotile cilia syndrome。此症候群包括三種病症：1)慢性鼻竇炎，2)支氣管擴張症，3)內臟反位。此病為自體隱性遺傳疾病，發生率約為1/15000~1/30000。病人常有慢性或反覆性的呼吸道感染，嗅覺障礙和不孕症，治療方式以症狀治療為主。本院歷1例Kartagener氏症候群之女性患者，因鼻竇炎來診，在施以內視鏡鼻竇手術後，症狀明顯改善。因此病例罕見，故提出報告。(中耳醫誌 1997;32:450-454)

關鍵字

Kartagener氏症候群 ； 慢性鼻竇炎 ； 內視鏡功能性鼻竇手術

並列摘要

Kartagener’s syndrome, also known as immotile cilia syndrome, is a rare syndrome presumed to be inherited as an autosomal recessive that characterized by chronic sinusitis, bronchiectasis, and situs inversus. It may also have signs of chronic or recurrent respiratory infection, anosmia or infertility. The statistics indicated one out of fifteen to thirty thousand people may be in risk of having this syndrome. The treatments for Kartagener’s syndrome are uniquely different. An “endoscopic sinus surgery”, was performed by us recently to a female patient with Kartagener’s syndrome who suffered from sinusitis. The result of this operation was very encouraging, a significant improvement of her condition was noted. We would like to report this rare case to our fellow physicians.

並列關鍵字

kartagener's syndrome ； chronic sinusitis ； functional endoscopic sinus surgery