透過您的圖書館登入
IP:3.142.134.99
  • 期刊
  • OpenAccess

Primary Pulmonary Myxoid Malignant Fibrous histiocytoma

原發性肺部黏液性惡性纖維組織瘤

摘要


肺部原發惡性纖維組織瘤(malignant fibrous histiocytoma)為罕見之肺部間質腫瘤,而黏液性(myxoid)變異形態更罕見。本案例報告一位年輕男性在胸部不適後卻意外發現一在胸部X光為非特異性巨大左肺腫塊,經左全肺切除後,病理免疫組織學檢查證實為罕見之肺臟原發惡性纖維組織瘤之黏液變異。術前肋間彩色都卜勒超音波為一異質性無血流之肺內囊性腫塊,電腦斷層則顯現一具壁上節結之囊性肺腫瘤,磁振造影發現更具組織特性的黏液狀訊號變化於囊內含物與腫瘤之胸壁侵犯。比較病理結果顯示,此種具囊性變化之原發性肺臟黏液惡性纖維組織瘤有特殊影像發現並具診斷價值。

並列摘要


Primary pulmonary malignant fibrous histiocytoma (MFH) is a rare mesenchymal neoplasm of the lung. Myxoid variant is an uncommon subtype of primary pulmonary MFH. In this report we present a case of a young adult who had chest discomfort and was found to have a huge mass in the left lung. Left pneumonectomy was performed and a myxoid variant of primary pulmonary MFH was proven by immunohistochemistry. Intercostal color-doppler ultrasound showed a heterogeneous cystic mass with internal echogenicity of the cystic content and thick wall but without obvious blood flow. The chest CT showed a huge cystic mass in the lung parenchyma with mural nodules. MRI demonstrated more findings then CT, including chest wall invasion and characteristic signal intensity of the cystic content compatible with mucin. The imaging findings of this myxoid variant or primary pulmonary sarcoma with cystic change were unique and correlated with pathologic diagnosis.

延伸閱讀