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Alport氏症候群－病例報告
Alport Syndrome-A Case Report
摘要
本文報告提出一例“ALPORT氏症候羣”患者，有典型的前圓錐狀及後圓錐狀水晶體(Anterior & Posterior Lentionus)及輕度品體囊下白內障。此外，病人有長久的聽力喪失及多年慢性腎衰竭，病人接受水晶體摘除術並裝置後房人工水晶體後，經過十個月的追踪治療，其眼部病變所造成的屈光變化可得到滿意的改善。
關鍵字
無資料並列摘要
Alport's syndrome is a hereditary disease characterized by progressive hemorrhagic nephritis and sensorineural hearing loss. The association of ocular abnormalities with Alport's syndrome was first reported by Sohar in 1956. We present a case of Alport's syndrome who has ant. & post. lenticonus & post. capsule opacity in both eyes. Chronic renal failure progressed requiring hemodialysis since 7 years ago. Progressive hearing loss has been noted since 20 years of age, as bilateral sensory hearing loss was confirmed by audiometry and a positive family history was noted, he is considered to be a typical case of Alport's syndrome. Since he was much troubled by his poor visual acuity in performing his daily activities, so we performed ECCE+IOL implantation trying to solve his problem. As expected, the highly myopic refractive error of lenticonus is much improved.
延伸閱讀
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