硬化性纖維瘤(侷限性漩渦狀纖維瘤)是一種罕見之腫瘤。它可以單獨發生或是 Cowden’s疾病的一種皮膚表現。扇大細胞膠原纖維瘤是一種罕見的新變型,於最近被提出。在病理組織學上除了典型的侷限性漩渦狀纖維瘤的表現,亦可見到散在性的多核巨大細胞。在此 我們報告一例於皮下組織的罕見變異型。
Sclerotic fibroma (Circumscribed storiform collagenoma) is a rare tumor. It may occur sporadically or in the context of Cowden’s disease. A new rare variant of giant cell collagenoma was recently described. The new variant showed scattered multinucleatd giant cells in an otherwise typical circumscribed storiform collagenoma. Herein, a case of this rare variant occurring in subcutis is reported.