孔洞腦症－17病例的臨床分析

馬偕醫院小兒科自72年9月至74年4月之間，共經歷17例大腦孔洞腦症的病例。其診斷除由臨床資料所見之外，並經電腦斷層攝影或扇形實時間顱部超音波的檢查而證實。大多數(70%)都是在嬰兒期卽較診察出來。性別分佈以男性佔多數（男：女=12:5）。臨床徵侯以局部運動障碍最常見(58.8%)，約三分之一的病例由於年齡尚小，追踪時間不夠長，臨床上並沒有明顯的症狀出現。分析其致病因素以新生兒顱內出血佔最多數，其次依序為新生兒窒息，顱部外傷，低血容性休克，先天性孔洞腦症，腦膜腦室炎；剩餘約四分之一的病例，未能追溯到。至於其好發的位置則以大腦頂葉和額葉為多。若僅就出血後孔洞腦囊腔而言，其好發位置則在枕業。在10例接受一年追踪檢查的病例當中，僅3例其精神運動發育尚稱正常。長期的追踪和預後有待吾人進一步的評估。

關鍵字

無資料

並列摘要

Seventeen cases of porencephaly were experienced from September 1983 to April 1985. All were proved by either CT brain scans or ultrasound sector scan. The majority (70%) of the cases were diagnosed by the first year of life. Male infants were predominant (M:F=12:5). Focal motor deficits, contralateral to the affected side, were the most common presenting features. The other clinical manifestations included seizures and delay of psychomotor development. However, about one-third of the cases have had no remarkable symptoms or signs to the present. The most frequent predisposing factors in our series were intracranial hemorrhages at the neonatal stage in seven cases, neonatal asphyxia in two cases, head injury in one case, hypovolemic shock in one case, congenital porencephaly in one case and central nervous system infection in one case. No definite etiology could be traced in the rest of four cases. Cysts were frequently found in the frontoparietal regions. As far as the post-hemorrhagic porencephaly was concerned, the occipital lobe was most frequently involved. None of the cases in this series showed progressive neurological deterioration, hemimacrocrania or mass effect; hence neurosurgical intervention was not considered. On the short-term follow-up of 10 cases, there were only 3 patients with normal psychomotor development. The long-term follow-up and prognosis remain for further evaluation.

並列關鍵字

porencephaly ； porencephalic cyst ； neonatal posthemorrhagic porencephaly

被引用紀錄

吳長鑫（2008）。浮接場板結構橫向雙擴散金氧半場效電晶體之最佳化設計〔碩士論文，國立清華大學〕。華藝線上圖書館。https://doi.org/10.6843/NTHU.2008.00701

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孔洞腦症－17病例的臨床分析

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