Congenital Horner's Syndrome: Report of One Case

先天性Horner's症候群：一病例報告

佘振興(Jenn-Shing Sher) ； 鄭志承(Chee-Chang Jang)

《Acta Paediatrica Sinica》 33卷2期 (1992/04) Pp. 144-147

摘要

先天性Horner's症候群是一種極爲少見，未明原因的頸部交感神經病變，主要臨床表徵爲患側臉部無汗，眼瞼下垂，縮瞳和虹膜異色，藥理試驗以4% Cocaine溶液和l:1000 Epinephrine溶液，或l% Hydroxyamphetamine溶液測試瞳孔反應，可以區別為神經節前病變或神經節後病變。本報告病例爲一足月，生産順利之男嬰，於出生後第二天發現右側眼瞼下垂，在哭泣或餵奶時，右側臉部無汗及無潮紅現象，眼部檢查發現右側瞳孔縮小，藥理瞳孔試驗結果為神經節後病變型，頭頸部和胸部放射線學檢查及頸部電腦斷層攝影檢查，均無異常發現，故診斷為先天性Horner's症候群，兒童期之Horner's症僞群，少數是併發於腫瘤或嚴重産傷，所以每個病例都必須經過詳細檢查，確定無腫瘤病灶，方可診斷爲先天性Horner's症候群，本症在本質上並不會造成嚴重的能力喪失，通常不需要治療。

並列摘要

Congenital Horner's syndrome is an infrequent illness caused by a lesion of the cervical sympathetic nerve fiber. It's clinical features are facial anhidrosis, ptosis, miosis, and hypochromia iridis of the affected side. The subject of this report, a full-term male newborn, had had a smooth birth process but was found on the second day of life to have narrowing of the palpebral fissure and absence of facial flushing on the right side when he cried. Ophthalmologic examination revealed a smaller right pupil. The above abnormalities proved to result from a post-ganglionic lesion, after pharmacologic test. Roentgenograms of the skull, chest and cervical spine were normal, and a computed tomography scan of the cervical spine showed no abnormalities. The diagnosis was of congenital Horner's syndrome. Since no congenital Horner's syndrome to the newborn period could be found in previous literature, this report is presented.

並列關鍵字

Congenital Horner's syndriome ； post-ganglionic lesion