Congenital tracheal stenosis remains a rare congenital anomaly. The presenting signs and symptoms are stridor, recurrent pneumonia and respiratory distress which are commonly seen in other diseases. The rarity of congenital tracheal stenosis and non-specific clinical presentation makes it a challenge for early diagnosis and appropriate treatment. A nine month-old infant presented with stridor and respiratory distress that failed to respond to dexamethasone. He was diagnosed as having class I tracheal stenosis by bronchoscopy and radiographic studies. The patient improved after conservative medical treatment. Though an uncommon diagnosis, further differentiating patients into one of three classes helps aid in treatment planning.