- 期刊
Intraabdominal and Retroperitoneal Lymphangiomas in Adults: Report of Six Cases
成人腹腔內及後腹腔淋巴管瘤：六病例報告
摘要
淋巴管瘤是一種好發於兒童，罕見的淋巴系統的先天性異常。約95%的淋巴血管瘤發生於頸部和腋下，而其他部位，包括腹腔的淋巴血管瘤佔的比率少於5%。腹腔內的淋巴血管瘤可能發生於腸繫膜、胃腸道、後腹腔、脾臟、肝臟和胰臟。我們分析六位腹腔內淋巴血管瘤成人病患的臨床表現、影像學特徵及治療成果。 研究方法採回朔性分析，2001年至2006年本院共治療六位腹腔內淋巴血管瘤病患，收集他們的病例紀錄、手術紀錄及病理資料。 六位病患性別分別為三位男性與三位女性。診斷時的平均年齡為38歲（由22歲至57歲）。臨床上主要的症狀為腹脹（2位）、腰痛（2位）及排便裹急後重（1位）。另一位病患術前並無症狀，在治療十二指腸腫瘤時於手術中意外發現。淋巴血管瘤分別發生於腸繫膜（2位）、後腹腔（2位）、空腸（1位）及脾臟（1位）。六位病患都接受手術將病灶完全切除，在平均追蹤2年（由2個月至4.5年）的期間內，都沒有復發的案例。 成人的腹腔內淋巴血管瘤屬於良性，且生長緩慢。它們在嬰兒時期就已經形成，但病程進展相當緩慢，可於成人時期才出現症狀。在診斷確立之後，應該儘早接受手術將病灶完全切除，因為疾病的預後相當的好。
關鍵字
無資料並列摘要
This study retrospectively reviewed the clinical features of intraabdominal and retroperitoneal lymphangiomas. We also evaluated the preoperative diagnosis, radiological features, surgical treatment and outcome of these rare tumors. Between 2001 and 2006, six patients underwent surgical resection of abdominal lymphangioma. The clinicopathological data were collected and the patients medical records, operative notes and pathology reports were reviewed. The age at diagnosis ranged from 22 to 57 years. The main clinical symptoms were abdominal distension (n=2), flank pain (n=2) and tenesmus (n=1). One patient was asymptomatic and incidentally detected during the laparotomy. The male-to-female ratio was 1:1. The abdominal lymphangiomas occurred in the mesentery (n=2), retroperitoneum (n=2), jejunum (n=1) and spleen (n=1). All six patients underwent complete surgical resection with or without organ resection, and there was no recurrence at a mean follow-up of two years (ranged from two months to 4.5 years). Adult type abdominal lymphangiomas are benign and indolent. They develop during fetal life and have a chronic history, and thus may present later in adulthood. A complete resection is suggested after the diagnosis is established, and gives a favorable prognosis.
延伸閱讀
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