- 期刊
Sjogren's Syndrome Manifested as Hypokalemic Paralysis
史格蘭氏症候群以低血鉀性癱瘓為起始表現
摘要
一名三十一歲女病患因低血鉀性癱瘓住院。其血液檢查呈高血氯性代謝性酸中毒而尿液檢查則發現有正向之陰離子間隙，診斷為遠端腎小管性酸血症(distal renal tubular acidosis)。患者也訴說有乾燥症的症狀，進一步作免疫學檢查診斷為史格蘭氏症候群(Sjogren's syndrome)。遠端性腎小管性酸血症的併發症包括可致命性的低血鉀，腎結石，慢性腎衰竭，生長遲緩及骨質軟化症。早期診斷及長期的鹼性鉀鹽補充可有效的預防上述合併症。
關鍵字
無資料並列摘要
A 31-year old woman was admitted for hypokalemic paralysis. Laboratory examination revealed hyperchloremic metabolic acidosis with a positive urinary anion gap compatible with distal renal tubular acidosis (DRTA). Her sicca symptom, as well as positive autoimmune studies pointed to the underlying cause as a case of Sjogren's syndrome. The complications of DRTA include life threatening hypokalemia, nephrolithiasis, chronic renal failure, growth retardation and osteomalacia. These co-morbidities can be avoided if the diagnosis is made early and life long potassium alkali salt replacement is maintained.
延伸閱讀
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