We report the magnetic resonance imaging (MRI) findings of a rare case of choroid plexus carcinoma (CPC) in a 2 year-old Chinese girl. MRI showed a large inhomogeneously enhanced tumor in the atrium of the right lateral ventricle with extraventricular invasion of the adjacent brain parenchyma. Cerebral angiography showed a right ventricular hypervascular tumor predominantly supplied by the right anterior and posterior choroidal arteries. To our knowledge, this is the first report of choroid plexus carcinoma in Taiwan.