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復發性多發軟骨炎併發葡萄膜炎、上鞏膜炎之病例報告

Uveitis and Episcleritis in Relapsing Polychondritis-Case Report

摘要


本篇報告一例次發性多發軟骨炎的病例。病人為一46歲女性,因兩眼紅痛3個月,及兩耳脹痛、灼熱感而來求診。經檢查有兩眼結膜炎、上鞏膜炎、虹彩炎、眼底黃斑部水腫、及眼底血管炎;全身檢查呈兩耳軟骨炎,鼻軟骨炎、呼吸道軟骨炎的病變。耳軟骨病理檢查可見,軟骨基質嗜鹼性染色消失,軟骨細胞核皺縮,軟骨週圍淋巴球及漿液球浸潤。結膜病理檢查可見,血管週圍發炎細胞浸潤。經使用秋水仙素(colchicines)及類固醇(prednisolone)治療後病情緩解,目前仍在門診繼續追蹤檢查。

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並列摘要


We presented a case of relapsing polychondritis in a 46-year-old female. The clinical manifestations are as follows: bilateral auricular chondritis, binocular conjunctivitis, episcleritis, iritis, macular edema, and suspected nasal chondritis, respiratory tract chondritis. Histopathology of auricular cartilage biopsy reveals loss of basophilia in the matrix, pyknotic nuclei, and perichondral lymphocyte, plasma cell infiltration. Histopathology of conjunctival biopsy reveals perivascular cellar infiltration.

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