Isolated Orbital Neurofibroma: Clinical Presentation and Differential Diagnosis

單獨只發生眼窩神經纖維瘤而沒有合併全身性的神經纖維瘤是很罕見的。本文報告一個這種案例並且說明我們的治療這個病人的經驗。一位27歲病人其左上眼窩中間的區域有一個無痛、可觸摸到的腫塊，時間已有一年。他並沒有外傷病史，也沒有家族史或其他的證據顯示有第一型的神經纖維瘤。眼睛檢查方面發現左眼球向下移位，電腦斷層顯示有一個實體腫瘤在左上眼窩。之後幫病人實施眼窩剖開探查術以及腫瘤切除。組織病理學檢查證實是一個局部的眼窩神經纖維瘤。本文作者要強調單獨只發生眼窩神經纖維瘤而沒有合併全身性的神經纖維瘤是很少見的，必須要利用影像診斷學及組織病理學仔細跟其他的眼窩腫瘤作鑑別診斷。

關鍵字

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並列摘要

Isolated orbital neurofibromas without systemic neurofibromatosis are extremely rare. We report one such case and describe our experience with this patient. A 27y/o male patient presented with painless, palpable mass located at the left medial upper orbital area for one year. He had no prior trauma history, family history or other evidence of neurofibromatosis type I. Ocular examination revealed downward displacement of the left globe while computed tomography identified a localized solid mass of the superior orbit. An anterior orbitotomy with tumor resection was performed afterward. Histopathological examination proved the mass to be a localized orbital neurofibroma. The authors emphasize that the unusual occurrence of localized neurofibroma in the orbit with the absence of systemic neurofibromatosis requires careful differentiation from other orbital tumors by radiographic and histopathological studies.

並列關鍵字

isolated orbital neurofibroma ； localized orbital neurofibroma ； differential diagnosis

國際替代計量

Isolated Orbital Neurofibroma: Clinical Presentation and Differential Diagnosis

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