本篇報告一例僅侵犯肺及骨之成人藍格罕士氏細胞組織球症之25歲男性。患者因非特異性之主訴至本院門診,因胸部X光之特徵而被疑有此症,後經開胸切片及病理檢查得到確定診斷。其治療方式當依其侵犯範圍及疾病臨床表現而定。本篇也強調其與較高之癌變發生率相關,後續定期追蹤之處置將做此考慮。
We herein report the case of a 25-year-old male with a rare disease: Langerhans cell histiocytosis in the form of an oligo-organic (lung and bone) involvement. The patient presented himself to our OPD with a non-specific complaint, and the radiologic findings prompted the suspicion of this diagnosis, which was later proved by open lung biopsy and pathology examinations. Treatment should be tailored to suit the extent of involvement and the clinical activity of the disease. The increased incidence of malignancy in patients with this disease is emphasized in this article, so the patient will be followed regularly and carefully.