摘要
卡波西樣血管內皮瘤是一種罕見、新近被描述的侵襲性血管腫瘤。在台灣尚未被報告過。我們在此報告一女童，於出生六週後，被發現在她的左足內側有一進行性之瘀青樣腫塊。各種治療，如類固醇、干擾素注射及雷射治療，均被嘗試過。然而，此血管性腫瘤仍舊展現持續生長之特性，造成左足及左小腿之巨大腫脹。之後，女童並出現Kasabach-Merritt徵候之併發症。截肢標本之病理檢查顯示卡波西氏肉瘤樣之血管增生及淋巴管樣血管腔之特徵。因此，我們診斷此女童為卡波西樣血管內膜瘤。截肢後，她的血小板數回復正常。術後追蹤至今，女童仍存活且無復發跡象。
關鍵字
無資料並列摘要
Kaposiform hemangioendothelioma is a recently described, rare, aggressive vascular tumor that has not been reported previously in Taiwan. We report a female baby who was noted to have a progressive, bluish mass over the medial side of the left foot at 6 weeks of age. Various therapies, including oral prednisolone, interferon-αand laser treatment were tried, but the vascular tumor still showed active proliferating behavior resulting in huge swelling of the left foot and left calf, and was complicated by Kasabach-Merritt phenomenon subsequently. Pathology of the amputation specimen revealed Kaposi’s sarcoma-like vascular proliferation and lymphatic-like vascular channels. A diagnosis of kaposiform hemangioendothelioma was made. After amputation, her platelet count returned to normal level. At present, she is still alive with no evidence of recurrence.
延伸閱讀
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