MRI in Evaluation of Heterotaxy Syndrome

內臟異位之磁振造影表徵

蔡伯邦(Po-Pang Tsai) ； 李覃(Tan Lee) ； 沈戊忠(Wu-Chung Shen)

《Mid-Taiwan Journal of Medicine》 3卷2期 (1998/06) Pp. 94-100

https://doi.org/10.6558/MTJM.1998.3(2).5

摘要

內臟異位係一種罕見先天性異常，常合併先天性心臟病，本文於1986年至1997年間搜集十個內臟異位之病例，年齡自19天至16歲不等，其中三例診斷為左同性質內臟異位，具有對稱性之長主支氣管，中斷性下腔靜脈，多發性脾臟及奇靜脈系統擴張之表徵，另七例診斷為右同質性內臟異位，則可發現對稱性之短主之氣管，同側性之主動脈與下腔靜脈，及先天性心臟異常，我們的結論為磁振造影係一種非侵入性之檢查工具，能提供心臟各種切面之影像，對於診斷、及外科手術、助益非淺。

關鍵字

內臟異位 ； 磁振造影

並列摘要

Visceral heterotaxy is a rare congenital malformation, often associated with congenital cardiac anomalies and abnormal viscero-atrial situs. A precise diagnosis must be made during early life so that the most appropriate treatment can be selected. Spin echo magnetic resonance (MR) findings in 10 patients with heterotaxy syndrome (7 with right isomerism, 3 left isomerism) were reviewed. The MR imaging (MRI) findings of the seven cases of visceral heterotaxy with right isomerism included eparterial bronchi (n=7), ipsilateral position of the abdominal aorta and inferior vena cava (IVC) (n=3), and prominent congenital cardiac anomaly (n=7), such as common atrioventricular canal (CAVC). The MRI findings of the three cases of heterotaxy with left isomerism included interruption of IVC (n=3), engorged azygos-hemiazygos system (n=3), and hyparterial bronchi (n=3). MRI can make it possible to have an accurate and non-invasive diagnosis on patients with heterotaxy syndrome.

並列關鍵字

heterotaxy syndrome ； MRI