- 期刊
Primary Endocardial Fibroelastosis with Dilated Cardiomyopathy: Report of One Case
心內膜彈力纖維增生症合併擴大型心肌病變：一病例報告
摘要
我們報告一個懷孕27周的早產兒，出生時就表現心臟肥大的症狀。胎兒時期心臟超音波顯示左心肥大。嬰兒在誕生後不久即呼吸窘迫和心臟衰竭。心臟超音波顯示擴大性心肌病變並且懷疑是心內膜彈力纖維增生症(endocardial fibroelastosis, EFE)。在升壓劑的使用之下，心衰竭仍繼續惡化。嬰兒於15天大時死於循環衰竭。病理解剖確認心內膜彈力纖維增生症的診斷。這個罕見病例告訴我們，心內膜彈力纖維增生症在胎兒期就可以表現心衰竭的症狀，不一定出生後一段時間才被發現。感染、代謝，以及自體免疫方面疾病都是有須要排除的病因。
並列摘要
We report a case of dilated cardiomyopathy presented in a premature infant of 27 weeks' gestational age. A prenatal sonography revealed left ventricular enlargement. The infant presented with respiratory distress and heart failure soon after birth. Echocardiograms performed after birth showed dilated cardiomyopathy, and endocardial fibroelastosis was suspected. Heart failure progressed despite administration of inotropic agents. The infant died after fifteen days from circulatory failure. Postmortem examination confirmed the diagnosis of endocardial fibroelastosis.
延伸閱讀
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