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Dental Treatment of a Child with Fibrodysplasia Ossificans Progressiva (FOP) under General Anesthesia: A Case Report

進化性骨化肌炎症病患的牙科治療:病例報告

摘要


進化性骨化肌炎(FOP)是一罕見的體染色體顯性遺傳疾病,特徵是先天性足部大拇趾型態異常以及漸進式的異位增生的骨質,使得患者漸漸不能動。在二十歲以前,進化性骨化肌炎的病童在當軟組織、肌肉的外傷時,都可能引發患者的肌肉腫脹發炎,而促進受傷部位發生骨化。因此在醫療處置及牙科治療上都需作特殊的考量,本文將報告一位三歲的進化性骨化肌炎患者所作的牙科治療與處置。

並列摘要


Fibrodyplasia ossificans progressive (FOP) is a rare disease caused by autosomal dominant disorder. It is characterized by congenital malformations of the great toes and progressive heterotopic endochondral ossification (HEO) that cause cumulative immobility. During the 1st decade of life, most children with FOP develop episodic inflammatory soft tissue swelling and later develop into ossification at injury site in response to soft tissue trauma and muscle damage. Special medical and dental consideration are needed to prevent injury or iatrogenic harm. Herein we report on the dental considerations and managements of a case of three-year-old case with fibrodysplasia ossificans progressiva.

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