多型性腺瘤癌(carcinoma ex pleomorphic adenoma, CXPA)為一種罕見的多形性腺瘤惡性轉變。其癌化風險因子包括:長時間的多型性腺瘤病史體積大、來自小型唾液腺,患者年紀大等等。由於多型性腺瘤癌發生率極低,其標準治療與預後尚未有定論。手術治療為現今的主要治療方式,對於有高風險因子的病人,可考慮術後放射治療。本文以一個44歲女性因20年的右側腮腺瘤病史,而來到門診接受手術治療,病理解剖發現有癌性轉化,因此藉由此案例,來回顧此疾病近期發展與治療。
Demasi AP, Furuse C, Soares AB, et al. Peroxiredoxin I, platelet-derived growth factor A, and platelet-derived growth factor receptor alpha are overexpressed in carcinoma ex pleomorphic adenoma: association with malignant transformation. Hum Pathol 2009;40:390-7.
Hsieh, C. Y., Chang, K. C., Lin, C. Y., Yu, Y. C., Roan, T. L., Chen, Y. S., & Lin, T. W. (2017). 惡性腫瘤合併手術轉移-案例報告及文獻回顧. 臺灣整形外科醫學會雜誌, 26(2), 232-237. https://www.airitilibrary.com/Article/Detail?DocID=a0000593-201706-201707250030-201707250030-232-237
Kuo, Y. C., Lee, J. J., Liu, C. C. H., Hong, R. L., & Chen, M. T. (2012). 腺泡狀軟組織肉瘤-案例報告及文獻回顧. 臺灣整形外科醫學會雜誌, 21(4), 351-358. https://doi.org/10.7096/TJTSPS.201212.0351
Wang, J. S., & Tseng, C. H. (1994). 肺部多形性腺瘤-病例報告及文獻回顧. The Kaohsiung Journal of Medical Sciences, 10(9), 522-527. https://doi.org/10.6452/KJMS.199409.0522
Liao, W. J., & Cho, D. Y. (2001). 多形性黃色星狀細胞瘤:─病例報告與文獻回顧. Mid-Taiwan Journal of Medicine, 6(4), 238-243. https://doi.org/10.6558/MTJM.2001.6(4).7